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Congenital glaucoma: literature review

https://doi.org/10.25700/NJG.2019.02.11

Abstract

Despite the rare incidence of childhood glaucoma in the routine practice of an ophthalmologist, the status of a disabling disease dictates the need to treat this group of patients as carefully and warily as possible. Difficulties with the diagnosis, the choice of the optimal treatment algorithm and the subsequent tactics of monitoring patients with pediatric glaucoma necessitated detailed coverage of this pathology with the accumulation and systematization of data from various sources. The review combines the concepts of etiology, pathogenesis, classification, and also focuses on diagnostic criteria and therapeutic approaches in the management of patients with pediatric glaucoma. The current data on the genetics of the disease are detailed, the underlying mechanisms for the development of glaucoma in children are highlighted, and various classification systems are also reviewed. International criteria for diagnosis are also included. Attention is drawn to the importance of choosing a pathogenetically substantiated surgical technique. The importance of timely verification of the diagnosis and promptly initiated treatment is emphasized. Despite the aggressiveness and refractory nature of the disease, it is possible, with promptly and adequately taken measures, to maintain sufficiently high visual functions for the patient to continue an independent lifestyle.

About the Authors

A. K. Lazareva
The S. Fyodorov Eye Microsurgery Federal State Institution, Novosibirsk department
Russian Federation

M.D.

10 Kolkhidskaya str.,Novosibirsk, Russian Federation, 630096



O. N. Kuleshova
The S. Fyodorov Eye Microsurgery Federal State Institution, Novosibirsk department; Novosibirsk State Medical University of Ministry of Health of the Russian Federation
Russian Federation

Med.Sc.D., Professor, Head of the Ophthalmology Department.

10 Kolkhidskaya str.,Novosibirsk, Russian Federation, 630096

52 Krasnyi prospect str., Novosibirsk, Russian Federation, 630091



S. V. Aidagulova
Novosibirsk State Medical University of Ministry of Health of the Russian Federation
Russian Federation

Ph.D. in Biological sciences, Professor.

52 Krasnyi prospect str., Novosibirsk, Russian Federation, 630091



V. V. Chernykh
The S. Fyodorov Eye Microsurgery Federal State Institution, Novosibirsk department
Russian Federation

Med.Sc.D., Professor, Director.

10 Kolkhidskaya str.,Novosibirsk, Russian Federation, 630096



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Lazareva A.K., Kuleshova O.N., Aidagulova S.V., Chernykh V.V. Congenital glaucoma: literature review. National Journal glaucoma. 2019;18(2):102-112. (In Russ.) https://doi.org/10.25700/NJG.2019.02.11

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